Stem cell transplantation in patients with severe congenital neutropenia with evidence of leukemic transformation
نویسندگان
چکیده
منابع مشابه
Stem cell transplantation in patients with severe congenital neutropenia without evidence of leukemic transformation.
Severe congenital neutropenia (CN) (Kostmann syndrome) is a hematologic disorder characterized by a maturation arrest of myelopoiesis at the promyelocyte/myelocyte stage of development. This arrest results in severe neutropenia leading to absolute neutrophil counts (ANC) below 0.2 x 10(9)/L associated with severe bacterial infections from early infancy. Data on over 300 patients with CN collect...
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15 صفحه اولIndications for hematopoietic cell transplantation for children with severe congenital neutropenia.
Severe congenital neutropenia (SCN) is a hematologic condition characterized by arrested maturation of myelopoiesis at the promyelocyte stage of development (1). With appropriate treatment using recombinant human granulocyte colony-stimulating factor (r-HuG-CSF), patients with SCN are now surviving well past infancy. With longer survival, the high risk of developing myelodysplastic syndrome (MD...
متن کاملprevention and control of infections in patients with severe congenital neutropenia; a follow up study
severe congenital neutropenia is one of primary immunodeficiency disorders that characterized by severe neutropenia and is associated with severe systemic bacterial infections from early infancy. granulocyte colony stimulating factor (gcsf) is clinically used as a treatment for congenital and acquired neutropenia. the aim of this study was evaluation of gcsf (pd- grastim) in treatme...
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ژورنال
عنوان ژورنال: Bone Marrow Transplantation
سال: 2005
ISSN: 0268-3369,1476-5365
DOI: 10.1038/sj.bmt.1704813